Cerebral sinus venous thrombosis (CSVT) is a rare and serious form of stroke, with an incidence rate accounting for 0.5% - 1% of all stroke cases. The annual incidence of CSVT ranges from 0.22 to 1.32 cases per 100,000 people. This condition can affect individuals of all ages, including children, and is notably more common in women, with a prevalence rate three times higher than that in men. However, the prevalence between genders becomes similar after the age of 60. The etiology of CSVT is multifactorial, with a range of risk factors involved. These risk factors can include both reversible and non-reversible causes, complicating the diagnosis and management of CSVT. Due to its rarity, early recognition of CSVT can be challenging, making awareness of clinical signs, symptoms, and predisposing conditions crucial for timely intervention. Given the potential for significant neurological impairment, understanding the risk factors and clinical manifestations is essential in improving outcomes for individuals affected by CSVT. This review discusses the incidence, epidemiology, risk factors, and clinical presentation of CSVT, with an emphasis on the need for early detection and effective management strategies